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síndRoMe de shoCK tóxiCo PoR stRePtoCoCCus PyoGenes
REVISTA MÉDICA DE ROSARIO 105
Introducción
La enfermedad invasiva por Streptococcus Pyogenes (S.
Pyogenes) puede presentarse en niños con un espectro
de manifestaciones que va desde cuadros de escasa sig-
nosintomatología inicial o con clínica inespecíca, hasta
formas graves de elevada morbimortalidad que requie-
ren cuidados intensivos.
1
La puerta de entrada suele ser
principalmente la piel, aunque puede no encontrarse el
foco primario de infección.
2,3
Entre los factores de riesgo
para su desarrollo se encuentran el pertenecer a edades
extremas (menos de 5 y más de 65 años), estados de
inmunosupresión, varicela y diabetes.
4
Entre las infecciones invasivas por S. Pyogenes se
encuentran la sepsis, celulitis, neumonía, osteomielitis
y artritis, que pueden asociarse a manifestaciones me-
diadas por toxinas, como la ebre escarlatina, la fascitis
necrotizante y el síndrome de shock tóxico (SST).
1
En la bibliografía internacional se ha informado un
incremento en las últimas décadas en la frecuencia de la
enfermedad invasiva por S. Pyogenes asociado a un au-
mento en la mortalidad, fundamentalmente relacionada
con el SST y la fascitis necrotizante.
5,6
En la Argentina
se evidenció una tasa de letalidad global en niños del
7,69%.
7
El SST por S. Pyogenes puede tener una evolución
muy rápida,
8
con una tasa de letalidad de entre el 35 y el
40%,
9
por lo que el manejo en urgencias adquiere una
importancia trascendental, con un diagnóstico precoz
de la infección, una adecuada selección del tratamiento
antibiótico y la implementación de medidas intensivas
de sostén.
10
El SST puede ocurrir junto con otras ma-
nifestaciones invasivas por S. Pyogenes, y se caracteriza
por ebre alta, hipotensión arterial de inicio rápido y
falla multiorgánica acelerada.
11
Puede estar precedido en
las 24 o 48 horas previas por síntomas inespecícos de
ebre, escalofríos, mialgias, náuseas, vómitos y diarrea,
y, de acuerdo a los criterios establecidos por e Working
Group on Severe Streptococcal Infections, el SST se diag-
nostica cuando se produce el aislamiento del germen
de un sitio normalmente estéril sumado a hipotensión
arterial, junto dos o más de los siguientes criterios: a) fa-
llo renal, b) coagulopatía, c) distrés respiratorio del tipo
adulto, d) erupción eritematosa diseminada que podía
descamar y e) fascitis necrotizante, miositis o gangrena.
1
La agresividad del S. Pyogenes puede vincularse a la
presencia de factores de virulencia, como la proteína M
o el factor de opacidad (FO) del suero, que, junto con
las exotoxinas pirógenas estreptocócicas (Spe), se aso-
cian al SST y a las otras formas graves.
8,9,12
Los serotipos
más frecuentes determinados por la proteína M, son los
M1 y M3,
5,13
y la tipicación de su gen codicador emm
constituye una herramienta epidemiológica para el estu-
dio de manifestaciones especícas.
11,14
A su vez, entre las
exotoxinas responsables de los cuadros invasivos graves
se encuentran las A, B, C, F, G, H, J, SSA y SMEZ.
15
Este artículo tiene el objetivo de aportar elementos
de valoración para la práctica pediátrica clínica, visibili-
zando la posibilidad de que un cuadro clínico inespecí-
co, con escasos síntomas y signos iniciales, puede de-
berse a una infección por S. Pyogenes, y que, pudiendo
pertenecer a cepas altamente virulentas, la probabilidad
de una evolución rápida y fatal es alta. En la medida que
pueda sospecharse con la mayor antelación este padeci-
miento podrán instrumentarse las medidas diagnósticas
y terapéuticas especícas que podrían ser cruciales para
salvar la vida del paciente.
Presentación del caso
Se presenta por guardia de efector hospitalario infan-
til una niña de 9 años de edad reriendo un cuadro de
ebre, vómitos y deposiciones líquidas desde la mañana
de ese día. Antecedentes médicos: parto normal, sin an-
tecedentes perinatales de jerarquía, bronquitis obstructiva
recurrente, internada en una oportunidad por fractura de
antebrazo. Al examen físico: talla 1,46 metros, peso 59
kg (índice de masa corporal 27,6), temperatura 38,7°C,
frecuencia cardíaca 110 latidos por minuto, frecuencia
respiratoria 38 por minuto, decaída, enoftálmica, len-
gua pastosa, mucosas pastosas, orofaringe rosada, bue-
na entrada bilateral de aire a la auscultación pulmonar,
ruidos netos y silencios libres a la auscultación cardíaca.
Abdomen globuloso, blando, depresible a la palpación,
doloroso a nivel difuso, con ruidos hidroaéreos positivos
a la auscultación abdominal. Se efectúan estudios de labo-
ratorio de ingreso con los siguientes resultados: glóbulos
rojos 5,7 millón/mm
3
, glóbulos blancos 26,1 mil/mm
3
,
hemoglobina 15 g%, hematocrito 45,3%, Volumen Cor-
puscular Medio 79, Hemoglobina Corpuscular Media
26,2, Concentración Hemoglobínica Corpuscular Me-
dia 33,1, recuento de plaquetas 372 mil/mm
3
, Fórmula
leucocitaria: neutrólos en cayado 0%/ neutrólos 96,3/
eosinólos 0%/ basólos 0%/ linfocitos 1,80%/ mono-
citos 1,90 %, Velocidad de Eritrosedimentación 2 mm/
hora, Calcemia total 9,8, Uremia 36 mg%, Glucemia
128 mg%, Estado Ácido Base: pH 7,34/ presión parcial
de oxígeno 32,6/ bicarbonato 17/ saturación de oxígeno